Postnatal management of a right or double aortic arch, Paediatrics

GGC Paediatric Guidelines
NHS GGC

Objectives

To identify children with a prenatal diagnosis of a right aortic arch (RAA) or double aortic arch (DAA) and to ensure a streamlined approach to postnatal investigation, treatment and follow up.

Scope

To ensure streamlined, multi disciplinary postnatal care for children with an antenatally detected right or double aortic arch.

Audience

Communication between prenatal and postnatal teams is vital to ensure a smooth transition from prenatal to postnatal life. Ensuring the appropriate investigations and follow up assessments are arranged.

 

Recommendations

  1. Parents should be offered prenatal genetic analysis
  2. Parents should be offered postnatal genetic analysis for 11 deletion
  3. Patients will be entered into PRAADA (retrospective) study
    1. As part  of  the  study  surveillance,  parents/clinicians  will  intermittently  be  provided  with  clinical questionnaires, to assess for any evidence of symptoms g. respiratory/ENT or dysphagia
  4. Prenatal Pathway Figure 1
  5. Postnatal Pathway Figure 2

 

Prenatal pathway

Prenatal pathway flowchart

Postnatal pathway

Postnatal pathway flowchart

Editorial Information

Last reviewed: 16/11/2021

Next review date: 30/11/2024

Author(s): Dr Lindsey Hunter.

Version: 3

Author email(s): lindsey.hunter@ggc.scot.nhs.uk.

Approved By: Paediatric Clinical Effectiveness & Risk Committee

References
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